중이염을 주소로 내원한 ANCA 음성 제한성 육아종증 다발 혈관염 1례

초록

Granulomatosis with polyangiitis(GPA) is a systemic disease that causes granulomatous inflammation and vasculitis to small to medium sized vessels. Although prompt diagnosis is vital for the successful treatment of the disease, it is often misdiagnosed as a simple inflammatory disease in ENT clinic. Anti-neutrophil cytoplasmic antibody(ANCA) tests positive in up to 90% of GPA, and it is a useful diagnostic marker for its strong association with the disease. However, we experienced ANCA-negative limited GPA presenting with intractable otitis media, thereby reporting this case with a brief review of the literature.

키워드