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Liver Cirrhosis Induced by Porphyria Cutanea Tarda: A Case Report and Review
- Lee, Kwang Gyun;
- Hyun, Jong Jin;
- Seo, Yeon Seok;
- Keum, Bora;
- Yim, Hyung Joon;
- ... Jeen, Yoon Tae;
- ... Lee, Hong Sik;
- ... Chun, Hoon Jai;
- ... Kim, Chang Duck;
- ... Ryu, Ho Sang;
- 외 1명
WEB OF SCIENCE
5SCOPUS
9초록
Porphyria cutanea tarda (PCT) is a metabolic disorder that results in a decrease in uroporphyrinogen decarboxylase activity. It is characterized by photosensitivity, bullae formation, and skin pigmentation. There are four types of PCT: acquired, familial, toxic, and hepatoerythropoietic. Uroporphyrin levels are elevated in the urine of PCT patients. PCT can be differentiated from other porphyrias by its clinical characteristics and the porphyrin levels in the serum, erythrocytes, urine, and feces. This metabolic disorder can lead to liver dysfunction as well as histological changes such as fatty infiltration or hepatic fibrosis. PCT rarely manifests as liver cirrhosis. We report herein a case of PCT-induced liver cirrhosis that progressed to hepatic failure. (Gut Liver 2010;4:551-555)
키워드
- 제목
- Liver Cirrhosis Induced by Porphyria Cutanea Tarda: A Case Report and Review
- 저자
- Lee, Kwang Gyun; Hyun, Jong Jin; Seo, Yeon Seok; Keum, Bora; Yim, Hyung Joon; Jeen, Yoon Tae; Lee, Hong Sik; Chun, Hoon Jai; Kim, Chang Duck; Ryu, Ho Sang; Um, Soon Ho
- 발행일
- 2010-12
- 유형
- Review
- 저널명
- Gut and Liver
- 권
- 4
- 호
- 4
- 페이지
- 551 ~ 555
- 언어
- ENG
- 출판사
- 거트앤리버 발행위원회
- 발행국가
- 대한민국
- 분량
- 5 페이지
- ISSN
- E 2005-1212
P 1976-2283