Diffuse Infiltrative Primary Cardiac Lymphoma with Delayed Extracardiac Involvement

초록

Primary cardiac lymphoma (PCL) is an extremely rare and fatal neoplasm of the heart. Traditionally, it is defined as lymphoma involving the heart or pericardium. PCL hasa poor prognosis because of the diagnostic difficulty and its location. We present thecase of a 48-year-old man who presented with pericardial effusion and diffuse cardiacwall thickening. We first suspected infiltrative heart disease. However, even after performinga biopsy, we could not establish an accurate diagnosis. After 20 months, primarycardiac diffuse large B cell lymphoma (DLBCL) was diagnosed by cervical lymphnode biopsy. In this case, after chemotherapy, the DLBCL lesions, including cardiacwall thickening, improved. The treatment outcome suggests that the diagnosis was diffuseinfiltrative PCL with delayed extracardiac involvement.

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