광응고술에 반응하지 않고 급속한 진행을 보인 선천성색소 결핍증 환아의 후극부 증식성 망막증 1 례

초록

A 11-days-old female was diagnosed as incontinentia pigmenti by skin biopsy was referred for ophthalmological examination.The fundus of the right eye showed vacularization only in the posteroir pole and neovascularization in the junctional area between vascular and avascula retina.Systemic evaluation revealed no associated abnormality.At 22 days of age, we ablated avascular retina with indirect diode laser photocoagulation under general anesthesia. Despite extensive 360 degree photocoagulation, fibrovascular proliferation was found to extend into vitreous cavity from optic disc 3 weeks after photocoagulation.

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