Maple syrup urine disease encephalopathy: a follow-up study in the acute stage using diffusion-weighted MRI
- Authors
- Ha, JS; Kim, TK; Eun, BL; Lee, HS; Lee, KY; Seol, HY; Cha, SH
- Issue Date
- Feb-2004
- Publisher
- SPRINGER
- Keywords
- brain; metabolic; maple syrup urine disease; diffusion-weighted MRI; neonate
- Citation
- PEDIATRIC RADIOLOGY, v.34, no.2, pp 163 - 166
- Pages
- 4
- Indexed
- SCIE
SCOPUS
- Journal Title
- PEDIATRIC RADIOLOGY
- Volume
- 34
- Number
- 2
- Start Page
- 163
- End Page
- 166
- URI
- https://scholarworks.korea.ac.kr/kumedicine/handle/2020.sw.kumedicine/20628
- DOI
- 10.1007/s00247-003-1058-7
- ISSN
- 0301-0449
1432-1998
- Abstract
- Neonatal maple syrup urine disease (MSUD) is associated with diffuse oedema and characteristic MSUD oedema. We present a newborn infant with two coexisting different types of oedema. The myelinated white matter showed a marked decrease in the water apparent diffusion coefficient (ADC) compatible with cytotoxic oedema. The unmyelinated white matter showed an increase in ADC, consistent with vasogenic-interstitial oedema. On follow-up studies, the cytotoxic oedema showed improvement, but the vasogenic-interstitial oedema progressed into brain atrophy.
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- Appears in
Collections - 2. Clinical Science > Department of Pediatrics > 1. Journal Articles
- 2. Clinical Science > Department of Radiology > 1. Journal Articles
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